Favilla, Vincenzo and Cimino, Sebastiano and Castelli, Tommaso and Marchese, Francesco and Russo, Giorgio Ivan and Russo, Marco and Madonia, Massimo and Morgia, Giuseppe (2012) Unusual presentation of tuberous sclerosis complex. Urology, Vol. 80 (4), e39-e40. eISSN 1527-9995. Article.
Full text not available from this repository.
A 47-year-old woman presented with acute abdominal pain, hematuria, signs of hemorrhagic shock and presence of a palpable mass in the right hypochondria at physical examination. Total body computed tomography showed bilateral renal angiomyolipoma (AML), voluminous abdominal mass of annexial origin, pulmonary lymphangioleiomyomatosis (LAM), and multiple subependymal calcification in the brain. After failure of selective transarterial embolization of the right kidney, the patient underwent exeresis of the abdominal mass and right nephrectomy (2200 g). This is a rare systemic manifestation of tuberous sclerosis complex consisting of renal AML and pulmonary LAM.
I documenti depositati in UnissResearch sono protetti dalle leggi che regolano il diritto d'autore
Repository Staff Only: item control page